{"id":8182,"date":"2023-02-22T00:00:00","date_gmt":"2023-02-21T23:00:00","guid":{"rendered":"https:\/\/instrid.sk\/uncategorized\/bruce-willis-ma-frontotemporalnu-demenciu-co-vieme-o-tejto-diagnoze\/"},"modified":"2023-02-22T00:00:00","modified_gmt":"2023-02-21T23:00:00","slug":"bruce-willis-ma-frontotemporalnu-demenciu-co-vieme-o-tejto-diagnoze","status":"publish","type":"post","link":"https:\/\/instrid.sk\/en\/archiv\/bruce-willis-ma-frontotemporalnu-demenciu-co-vieme-o-tejto-diagnoze\/","title":{"rendered":"Bruce Willis m\u00e1 frontotempor\u00e1lnu demenciu &#8211; \u010do vieme o tejto diagn\u00f3ze?"},"content":{"rendered":"<p><strong>Rodina Bruca Willisa predned\u00e1vnom ozn\u00e1mila, \u017ee 67-ro\u010dn\u00fd b\u00fdval\u00fd americk\u00fd herec trp\u00ed frontotempor\u00e1lnou demenciou (FTD). Vlani mu diagnostikovali af\u00e1ziu, ktor\u00e1 sp\u00f4sobuje probl\u00e9my s jazykom a re\u010dou. Af\u00e1zia vznik\u00e1 z r\u00f4znych pr\u00ed\u010din, naj\u010dastej\u0161ie po cievnej mozgovej pr\u00edhode. V pr\u00edpade Willisa je v\u0161ak teraz jasn\u00e9, \u017ee jeho \u0165a\u017ekosti s hovoren\u00edm boli prvotn\u00fdmi pr\u00edznakmi tejto obzvl\u00e1\u0161\u0165 \u0165a\u017ekej formy demencie.<\/strong><\/p>\n<h2>Bruce Willis<\/h2>\n<p>Frontotempor\u00e1lna demencia je stre\u0161n\u00fd term\u00edn pre v\u0161etky choroby, ktor\u00e9 sp\u00f4sobuj\u00fa <strong>postupn\u00fa stratu mozgov\u00e9ho tkaniva<\/strong> v prednej a postrann\u00fdch \u010dastiach mozgu. Aj ke\u010f ide o <strong>pomerne zriedkav\u00e9 ochorenie<\/strong>, je jedn\u00fdm z <strong>naj\u010dastej\u0161\u00edch d\u00f4vodov<\/strong> vzniku <strong>demencie<\/strong> u \u013eud\u00ed vo veku <strong>do 65 rokov<\/strong>. Na svedom\u00ed m\u00e1 pribli\u017ene <strong>40 percent pr\u00edpadov v tejto vekovej kateg\u00f3rii<\/strong>, uv\u00e1dzaj\u00fa \u0161t\u00fadie dostupn\u00e9 na port\u00e1loch sciencedirect.com a thieme-connect.com.<\/p>\n<p>Tento stav m\u00e1 aj \u010fal\u0161ie pomenovania &#8211; Pickova choroba, front\u00e1lna demencia, s\u00e9mantick\u00e1 demencia \u010di prim\u00e1rna progres\u00edvna af\u00e1zia. Vyv\u00edja sa pomaly, nieko\u013eko rokov. N\u00e1rast abnorm\u00e1lnych prote\u00ednov zasahuje <strong>k\u013e\u00fa\u010dov\u00e9 oblasti v mozgu<\/strong> a za n\u00e1sledok m\u00e1 <strong>zmeny spr\u00e1vania, osobnosti a re\u010dov\u00e9ho prejavu<\/strong>. Na rozdiel od in\u00fdch druhov demencie, ako je napr\u00edklad Alzheimerova choroba, nast\u00e1va <strong>strata pam\u00e4te<\/strong> a\u017e <strong>v neskor\u0161ej f\u00e1ze<\/strong> ochorenia.<\/p>\n<p style=\"text-align: center\"><em><strong>Ilustra\u010dn\u00fd obr\u00e1zok. Zdroj: unsplash.com<\/strong><\/em><\/p>\n<h3>Sympt\u00f3my<\/h3>\n<p>Existuj\u00fa <strong>tri rozdielne varianty<\/strong> frontotempor\u00e1lnej demencie. Ka\u017ed\u00fd z nich sa najprv prejavuje odli\u0161ne a je mo\u017en\u00e9 <strong>pom\u00fdli\u0165 si ich<\/strong> s in\u00fdmi diagn\u00f3zami. Prv\u00fd variant zapr\u00ed\u010di\u0148uje <strong>zmeny spr\u00e1vania<\/strong>, najm\u00e4 to, ako \u010dlovek <strong>kon\u00e1 v spolo\u010densk\u00fdch situ\u00e1ci\u00e1ch<\/strong>. Pacienti <strong>str\u00e1caj\u00fa takt<\/strong> a m\u00f4\u017eu robi\u0165 <strong>un\u00e1hlen\u00e9 rozhodnutia<\/strong>. M\u00f4\u017eu sa aj spr\u00e1va\u0165 nevhodne, napr\u00edklad d\u00e1va\u0165 sexu\u00e1lne n\u00e1vrhy. U niektor\u00fdch sa objavuj\u00fa fanatick\u00e9 ritu\u00e1lne spr\u00e1vanie \u010di \u00fapln\u00e1 strata empatie a starostlivosti.<\/p>\n<p>Tieto sympt\u00f3my poukazuj\u00fa na <strong>po\u0161kodenie predn\u00fdch lalokov<\/strong>, \u010dasti mozgu, ktor\u00e1 ur\u010duje na\u0161e spr\u00e1vanie, kontroluje na\u0161e impulzy, ovl\u00e1da na\u0161e em\u00f3cie a riadi re\u010d a pohyb. Ke\u010f predn\u00e9 laloky <strong>prestan\u00fa fungova\u0165<\/strong>, \u013eudia <strong>prich\u00e1dzaj\u00fa o schopnos\u0165 sebareflexie<\/strong> a pozorovania toho, ako sa zmenili. Mimoriadne n\u00e1ro\u010dn\u00e9 je to pre ich bl\u00edzkych, ktor\u00ed sa s pacientmi nem\u00f4\u017eu \u00faprimne porozpr\u00e1va\u0165, preto\u017ee t\u00ed nerozumej\u00fa tomu, kde je probl\u00e9m.<\/p>\n<p>\u0164a\u017ek\u00e9 je aj ur\u010denie diagn\u00f3zy, <strong>rovnak\u00e9 sympt\u00f3my<\/strong> sa vyskytuj\u00fa aj <strong>pri in\u00fdch ochoreniach<\/strong>, ke\u010f doch\u00e1dza k po\u0161kodeniu predn\u00fdch lalokov (cievne mozgov\u00e9 pr\u00edhody, n\u00e1dory). D\u00f4le\u017eit\u00e9 s\u00fa <strong>sn\u00edmky mozgu<\/strong> and <strong>kompletn\u00e1 zdravotn\u00e1 dokument\u00e1cia<\/strong>. Aby to mali lek\u00e1ri e\u0161te zlo\u017eitej\u0161ie, choroba sa v mnohom <strong>podob\u00e1 na viacer\u00e9 psychiatrick\u00e9 poruchy<\/strong>, ako s\u00fa napr\u00edklad depresia, schizofr\u00e9nia a obsedantno-kompulz\u00edvna porucha. Najm\u00e4 v po\u010diato\u010dn\u00fdch \u0161t\u00e1di\u00e1ch to m\u00f4\u017ee vies\u0165 k <strong>nespr\u00e1vnym diagn\u00f3zam<\/strong>.<\/p>\n<h3>G\u00e9ny d\u00e1vaj\u00fa n\u00e1dej<\/h3>\n<p>Nie je zn\u00e1me, <strong>ktor\u00fd z variantov<\/strong> diagnostikovali Willisovi, ale jeho rodina informovala, \u017ee prvotn\u00e9 pr\u00edznaky s\u00faviseli s <strong>\u0165a\u017ekos\u0165ami s re\u010dou<\/strong>. To zv\u00e4\u010d\u0161a poukazuje na n\u00e1beh \u010fal\u0161\u00edch dvoch variantov. V t\u00fdchto pr\u00edpadoch doch\u00e1dza k <strong>postupnej strate schopnosti hovori\u0165 a porozumie\u0165 jazyku<\/strong>. Ako choroba postupuje, <strong>odumieraj\u00fa mozgov\u00e9 bunky<\/strong> v predn\u00fdch a postrann\u00fdch lalokoch. Nez\u00e1le\u017e\u00ed na variante, pacienti napokon za\u017eij\u00fa <strong>v\u00e4\u010d\u0161inu<\/strong> spomenut\u00fdch <strong>sympt\u00f3mov<\/strong>. K nim sa pripoja probl\u00e9my s ch\u00f4dzou a pohybom. Ku koncu u\u017e mnoh\u00ed nedok\u00e1\u017eu jes\u0165 a preh\u013ata\u0165.<\/p>\n<p>Frontotempor\u00e1lna demencia je zdrvuj\u00faca diagn\u00f3za, ktor\u00e1 zmen\u00ed \u017eivot. <strong>Je nevylie\u010dite\u013en\u00e1 a lie\u010dba pom\u00e1ha len ve\u013emi m\u00e1lo.<\/strong> V s\u00fa\u010dasnosti sa kladie d\u00f4raz na <strong>zvl\u00e1danie pr\u00edznakov a maximaliz\u00e1ciu kvality \u017eivota<\/strong>. Pacientom sa pom\u00e1ha so zvl\u00e1dan\u00edm ich em\u00f3ci\u00ed a spr\u00e1vania, pod\u00e1vaj\u00fa sa antidepres\u00edva a antipsychot\u00edk\u00e1.<\/p>\n<p>Je tu v\u0161ak aj <strong>n\u00e1dej<\/strong>. Vedci pokro\u010dili v uplynul\u00fdch rokoch v pochopen\u00ed toho, <strong>ktor\u00e9 mozgov\u00e9 bunky s\u00fa zasiahnut\u00e9<\/strong>. Jeden z \u00f4smich pacientov m\u00e1 frontotempor\u00e1lnu demenciu v rodine, d\u00f4le\u017eit\u00e9 stopy k pochopeniu ochorenia s\u00fa v <strong>detailnej anal\u00fdze genetiky<\/strong>. Teraz bude podstatn\u00e9 <strong>prenies\u0165 v\u00fdskum do skor\u0161ej a kvalitnej\u0161ej diagnostiky a v\u00fdvoja liekov<\/strong>, ktor\u00e9 zastavia alebo zvr\u00e1tia t\u00fato devastuj\u00facu chorobu.<\/p>\n<p style=\"text-align: center\"><em><strong>Bruce Willis. Zdroj: pixabay.com<\/strong><\/em><\/p>\n<h3>Stanovisko rodiny<\/h3>\n<p>\u201eAko rodina by sme sa chceli v\u0161etk\u00fdm po\u010fakova\u0165 za podporu a s\u00facit pre Bruca za uplynul\u00fdch desa\u0165 mesiacov. Va\u0161a \u0161tedros\u0165 ducha je \u00fa\u017easn\u00e1 a sme za \u0148u nesmierne v\u010fa\u010dn\u00ed. Vieme, \u017ee m\u00e1te Bruca radi rovnako ako my, a preto by sme v\u00e1m chceli poskytn\u00fa\u0165 nov\u00e9 inform\u00e1cie. <em><strong>Odkedy sme na jar 2022 ozn\u00e1mili diagn\u00f3zu af\u00e1zie, Brucov stav pokro\u010dil. U\u017e m\u00e1me \u0161pecifickej\u0161iu diagn\u00f3zu: frontotempor\u00e1lna demencia (zn\u00e1ma ako FTD). Nane\u0161\u0165astie, \u0165a\u017ekosti s re\u010dou s\u00fa len jedn\u00fdm zo sympt\u00f3mov ochorenia, ktor\u00fdm trp\u00ed Bruce. Je to bolestiv\u00e9, ale je aj \u00fa\u013eava, \u017ee m\u00e1me jasn\u00fa diagn\u00f3zu.\u201d<\/strong><\/em><\/p>\n<p>&nbsp;<\/p>\n<p><em><strong>Zdroje: theconversation.com, theaftd.org<\/strong><\/em><\/p>\n<p><em><strong>Zdroj titulnej fotografie: pixabay.com<\/strong><\/em><\/p>","protected":false},"excerpt":{"rendered":"<p>Rodina Bruca Willisa predned\u00e1vnom ozn\u00e1mila, \u017ee 67-ro\u010dn\u00fd b\u00fdval\u00fd americk\u00fd herec trp\u00ed frontotempor\u00e1lnou demenciou (FTD). Vlani mu diagnostikovali af\u00e1ziu, ktor\u00e1 sp\u00f4sobuje probl\u00e9my s jazykom a re\u010dou.<\/p>","protected":false},"author":1,"featured_media":0,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[51],"tags":[],"class_list":["post-8182","post","type-post","status-publish","format-standard","hentry","category-archiv","two-columns"],"_links":{"self":[{"href":"https:\/\/instrid.sk\/en\/wp-json\/wp\/v2\/posts\/8182","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/instrid.sk\/en\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/instrid.sk\/en\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/instrid.sk\/en\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/instrid.sk\/en\/wp-json\/wp\/v2\/comments?post=8182"}],"version-history":[{"count":0,"href":"https:\/\/instrid.sk\/en\/wp-json\/wp\/v2\/posts\/8182\/revisions"}],"wp:attachment":[{"href":"https:\/\/instrid.sk\/en\/wp-json\/wp\/v2\/media?parent=8182"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/instrid.sk\/en\/wp-json\/wp\/v2\/categories?post=8182"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/instrid.sk\/en\/wp-json\/wp\/v2\/tags?post=8182"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}